Diseases

Neurofibromatoses

A group of disorders characterized by an autosomal dominant pattern of inheritance with high rates of spontaneous mutation and multiple neurofibromas or neurilemmomas. NEUROFIBROMATOSIS 1 (generalized neurofibromatosis) accounts for approximately 95% of cases, although multiple additional subtypes (e.g., NEUROFIBROMATOSIS 2, neurofibromatosis 3, etc.) have been described. (From Neurochirurgie 1998 Nov;44(4):267-72)

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A group of disorders characterized by an autosomal dominant pattern of inheritance with high rates of spontaneous mutation and multiple neurofibromas or neurilemmomas. NEUROFIBROMATOSIS 1 (generalized neurofibromatosis) accounts for approximately 95% of cases, although multiple additional subtypes (e.g., NEUROFIBROMATOSIS 2, neurofibromatosis 3, etc.) have been described. (From Neurochirurgie 1998 Nov;44(4):267-72)

MeSH Record

Classification

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MeSH Record

Synonyms

14 entry terms
  • Multiple Neurofibromas
  • Neurofibromatosis
  • Neurofibromatosis Syndrome
  • Multiple Neurofibroma
  • Neurofibroma, Multiple
  • Neurofibromas, Multiple
  • Neurofibromatosis Syndromes
  • Syndrome, Neurofibromatosis
  • Syndromes, Neurofibromatosis
  • Neurofibromatosis 3
  • Neurofibromatosis Type 3
  • Neurofibromatosis 3s
  • Neurofibromatosis Type 3s
  • Type 3, Neurofibromatosis

MeSH Record

Aspects Covered

35 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

Indexing Annotation

multiple neurofibromas; specifics are available

MeSH Record

History Note

2000(1993)

MeSH Hierarchy

Tree Numbers

MeSH Record

NLM Classification

QZ 380

AMA Style

References

  1. National Library of Medicine. Neurofibromatoses. Medical Subject Headings (MeSH). 2026. Unique ID D017253. http://id.nlm.nih.gov/mesh/2026/D017253
  2. Neurofibromatoses. In: Wikipedia. https://en.wikipedia.org/wiki/Neurofibromatosis
  3. Neurofibromatoses. In: Wikidata. https://www.wikidata.org/wiki/Q847605