Structured Summary
Abstract
An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN.
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Classification
Broader headings
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MeSH Record
Synonyms
17 entry terms
- 4-Trimethylaminobutyrate, 2-Oxoglutarate Oxygen Oxidoreductase (3-Hydroxylating)
- Butyrobetaine Hydroxylase
- Trimethylaminobutyrate Hydroxylase
- gamma-Butyrobetaine Hydroxylase
- gamma-Butyrobetaine, 2-Oxoglutarate Dioxygenase
- gamma-Butyrobetaine,2-Oxoglutarate Dioxygenase
- 2-Oxoglutarate Dioxygenase gamma-Butyrobetaine
- Dioxygenase gamma-Butyrobetaine, 2-Oxoglutarate
- Dioxygenase, gamma-Butyrobetaine
- Dioxygenase, gamma-Butyrobetaine,2-Oxoglutarate
- Hydroxylase, Butyrobetaine
- Hydroxylase, Trimethylaminobutyrate
- Hydroxylase, gamma-Butyrobetaine
- gamma Butyrobetaine Dioxygenase
- gamma Butyrobetaine Hydroxylase
- gamma Butyrobetaine, 2 Oxoglutarate Dioxygenase
- gamma Butyrobetaine,2 Oxoglutarate Dioxygenase
MeSH Record
Aspects Covered
29 allowable subheadings
Indexed with the subheadings administration & dosage, adverse effects, analysis, antagonists & inhibitors, biosynthesis, blood, cerebrospinal fluid, chemical synthesis, chemistry, classification, deficiency, drug effects, economics, genetics, history, immunology, isolation & purification, metabolism, pharmacokinetics, pharmacology, physiology, poisoning, radiation effects, standards, supply & distribution, therapeutic use, toxicity, ultrastructure, urine.
MeSH Record
History Note
2006(1980); use KETOGLUTARIC ACID 1973-1974, BETAINE 1972-1979, BUTYRATES 1974-1979, & AMINOBUTYRIC ACID 1970-1974
MeSH Hierarchy
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AMA Style
References
- National Library of Medicine. gamma-Butyrobetaine Dioxygenase. Medical Subject Headings (MeSH). 2026. Unique ID D050563. http://id.nlm.nih.gov/mesh/2026/D050563
- gamma-Butyrobetaine Dioxygenase. In: Wikidata. https://www.wikidata.org/wiki/Q3266583