Diseases

Porokeratosis

A heritable disorder of faulty keratinization characterized by the proliferation of abnormal clones of KERATINOCYTES and lesions showing varying atrophic patches surrounded by an elevated, keratotic border. These keratotic lesions can progress to overt cutaneous neoplasm. Several clinical variants are recognized, including porokeratosis of Mibelli, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis, and punctate porokeratosis.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A heritable disorder of faulty keratinization characterized by the proliferation of abnormal clones of KERATINOCYTES and lesions showing varying atrophic patches surrounded by an elevated, keratotic border. These keratotic lesions can progress to overt cutaneous neoplasm. Several clinical variants are recognized, including porokeratosis of Mibelli, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis, and punctate porokeratosis.

MeSH Record

Classification

Related Concepts

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MeSH Record

Synonyms

19 entry terms
  • Disseminated Superficial Actinic Porokeratosis
  • Keratoderma Palmoplantar, Punctate Type 2
  • Porokeratosis Palmaris et Plantaris Disseminata
  • Porokeratosis Plantaris Palmaris et Disseminata
  • Porokeratosis Plantaris, Palmaris, Et Disseminata
  • Porokeratosis of Mibelli
  • Porokeratosis, Disseminated Superficial Actinic
  • Porokeratosis, Disseminated Superficial Actinic 2
  • Porokeratosis, Disseminated Superficial Actinic, 2
  • Porokeratosis, Linear
  • Porokeratosis, Mibelli
  • Porokeratosis, Palmar, Plantar, And Disseminated 1
  • Porokeratosis, Palmoplantar
  • Porokeratosis, Punctate
  • Type 2 Punctate PPK
  • Linear Porokeratosis
  • Mibelli Porokeratosis
  • Palmoplantar Porokeratosis
  • Punctate Porokeratosis

MeSH Record

Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

Indexing Annotation

do not confuse with PARAKERATOSIS

MeSH Record

History Note

93

MeSH Record

Previous Indexing

  • Keratosis (1966-1992)

MeSH Hierarchy

Tree Numbers

AMA Style

References

  1. National Library of Medicine. Porokeratosis. Medical Subject Headings (MeSH). 2026. Unique ID D017499. http://id.nlm.nih.gov/mesh/2026/D017499
  2. Porokeratosis. In: Wikipedia. https://en.wikipedia.org/wiki/Porokeratosis
  3. Porokeratosis. In: Wikidata. https://www.wikidata.org/wiki/Q7230264