Structured Summary
Abstract
An enzyme of the oxidoreductase class that catalyzes the formation of L-TYROSINE, dihydrobiopterin, and water from L-PHENYLALANINE, tetrahydrobiopterin, and oxygen. Deficiency of this enzyme may cause PHENYLKETONURIAS and PHENYLKETONURIA, MATERNAL. EC 1.14.16.1.
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Classification
Broader headings
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See Also
MeSH Record
Synonyms
7 entry terms
- Phenylalanine 4-Hydroxylase
- Phenylalanine 4-Monooxygenase
- 4-Hydroxylase, Phenylalanine
- 4-Monooxygenase, Phenylalanine
- Hydroxylase, Phenylalanine
- Phenylalanine 4 Hydroxylase
- Phenylalanine 4 Monooxygenase
MeSH Record
Aspects Covered
29 allowable subheadings
Indexed with the subheadings administration & dosage, adverse effects, analysis, antagonists & inhibitors, biosynthesis, blood, cerebrospinal fluid, chemical synthesis, chemistry, classification, deficiency, drug effects, economics, genetics, history, immunology, isolation & purification, metabolism, pharmacokinetics, pharmacology, physiology, poisoning, radiation effects, standards, supply & distribution, therapeutic use, toxicity, ultrastructure, urine.
MeSH Record
Indexing Annotation
/defic: consider also PHENYLKETONURIAS and PHENYLKETONURIA, MATERNAL
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History Note
73(71)
MeSH Record
Previous Indexing
- Hydroxylases (1966-1970)
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AMA Style
References
- National Library of Medicine. Phenylalanine Hydroxylase. Medical Subject Headings (MeSH). 2026. Unique ID D010651. http://id.nlm.nih.gov/mesh/2026/D010651
- Phenylalanine Hydroxylase. In: Wikipedia. https://en.wikipedia.org/wiki/Phenylalanine_hydroxylase
- Phenylalanine Hydroxylase. In: Wikidata. https://www.wikidata.org/wiki/Q420604