Structured Summary
Abstract
Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown.
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Classification
Broader headings
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MeSH Record
Synonyms
13 entry terms
- Degos Disease
- Degos Syndrome
- Degos's Malignant Atrophic Papulosis
- Kohlmeier-Degos Disease
- Papulosis, Malignant Atrophic
- Atrophic Papuloses, Malignant
- Atrophic Papulosis, Malignant
- Disease, Degos
- Disease, Kohlmeier-Degos
- Malignant Atrophic Papuloses
- Papuloses, Malignant Atrophic
- Syndrome, Degos
- Erythrokeratoderma en cocardes
MeSH Record
Aspects Covered
35 allowable subheadings
Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.
MeSH Record
Indexing Annotation
malignant does not refer to neoplasm; do not confuse with the neoplasm ACANTHOMA, DEGOS see ACANTHOMA
MeSH Record
History Note
2008
MeSH Hierarchy
Tree Numbers
AMA Style
References
- National Library of Medicine. Malignant Atrophic Papulosis. Medical Subject Headings (MeSH). 2026. Unique ID D054853. http://id.nlm.nih.gov/mesh/2026/D054853
- Malignant Atrophic Papulosis. In: Wikipedia. https://en.wikipedia.org/wiki/Degos_disease
- Malignant Atrophic Papulosis. In: Wikidata. https://www.wikidata.org/wiki/Q911136