Diseases

Hypophosphatasia

A genetic metabolic disorder resulting from serum and bone alkaline phosphatase deficiency leading to hypercalcemia, ethanolamine phosphatemia, and ethanolamine phosphaturia. Clinical manifestations include severe skeletal defects resembling vitamin D-resistant rickets, failure of the calvarium to calcify, dyspnea, cyanosis, vomiting, constipation, renal calcinosis, failure to thrive, disorders of movement, beading of the costochondral junction, and rachitic bone changes. (From Dorland, 27th ed)

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A genetic metabolic disorder resulting from serum and bone alkaline phosphatase deficiency leading to hypercalcemia, ethanolamine phosphatemia, and ethanolamine phosphaturia. Clinical manifestations include severe skeletal defects resembling vitamin D-resistant rickets, failure of the calvarium to calcify, dyspnea, cyanosis, vomiting, constipation, renal calcinosis, failure to thrive, disorders of movement, beading of the costochondral junction, and rachitic bone changes. (From Dorland, 27th ed)

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Synonyms

1 entry terms
  • Hypophosphatasias

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Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

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Indexing Annotation

defic of blood phosphatases; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES

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History Note

72(66)

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AMA Style

References

  1. National Library of Medicine. Hypophosphatasia. Medical Subject Headings (MeSH). 2026. Unique ID D007014. http://id.nlm.nih.gov/mesh/2026/D007014
  2. Hypophosphatasia. In: Wikipedia. https://en.wikipedia.org/wiki/Hypophosphatasia
  3. Hypophosphatasia. In: Wikidata. https://www.wikidata.org/wiki/Q1313510