Diseases

Hyperlipoproteinemia Type III

An autosomal recessively inherited disorder characterized by the accumulation of intermediate-density lipoprotein (IDL or broad-beta-lipoprotein). IDL has a CHOLESTEROL to TRIGLYCERIDES ratio greater than that of VERY-LOW-DENSITY LIPOPROTEINS. This disorder is due to mutation of APOLIPOPROTEINS E, a receptor-binding component of VLDL and CHYLOMICRONS, resulting in their reduced clearance and high plasma levels of both cholesterol and triglycerides.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

An autosomal recessively inherited disorder characterized by the accumulation of intermediate-density lipoprotein (IDL or broad-beta-lipoprotein). IDL has a CHOLESTEROL to TRIGLYCERIDES ratio greater than that of VERY-LOW-DENSITY LIPOPROTEINS. This disorder is due to mutation of APOLIPOPROTEINS E, a receptor-binding component of VLDL and CHYLOMICRONS, resulting in their reduced clearance and high plasma levels of both cholesterol and triglycerides.

MeSH Record

Classification

Related Concepts

Knowledge Graph

Loading graph…

Drag nodes to rearrange; hover to trace links; click a node to open its page.

MeSH Record

Synonyms

16 entry terms
  • Broad Beta Disease
  • Dysbetalipoproteinemia
  • Dysbetalipoproteinemia, Familial
  • Familial Dysbetalipoproteinemia
  • Familial Hypercholesterolemia with Hyperlipemia
  • Hyperlipoproteinemia, Broad-beta
  • Hyperlipoproteinemia, Type III
  • Broad-beta Hyperlipoproteinemia
  • Hyperlipoproteinemia, Broad beta
  • Hyperlipoproteinemias, Type III
  • Type III Hyperlipoproteinemia
  • Type III Hyperlipoproteinemias
  • Autosomal Recessive Hypercholesterolemia
  • Hypercholesterolemia, Autosomal Recessive
  • Autosomal Recessive Hypercholesterolemias
  • Recessive Hypercholesterolemia, Autosomal

MeSH Record

Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

History Note

1980; for AUTOSOMAL RECESSIVE HYPERCHOLESTEROLEMIA use HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA 2022

MeSH Record

Previous Indexing

  • Hyperlipidemia/familial & genetic (1966-1979)

MeSH Hierarchy

Tree Numbers

AMA Style

References

  1. National Library of Medicine. Hyperlipoproteinemia Type III. Medical Subject Headings (MeSH). 2026. Unique ID D006952. http://id.nlm.nih.gov/mesh/2026/D006952
  2. Hyperlipoproteinemia Type III. In: Wikipedia. https://en.wikipedia.org/wiki/Familial_dysbetalipoproteinemia
  3. Hyperlipoproteinemia Type III. In: Wikidata. https://www.wikidata.org/wiki/Q2069207