Structured Summary
Abstract
A congenital condition where the greater portions of the cerebral hemispheres and CORPUS STRIATUM are replaced by CSF and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (Menkes, Textbook of Child Neurology, 5th ed, p307)
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Synonyms
7 entry terms
- Absence of Cerebral Hemispheres, Congenital
- Cerebral Hemispheres, Absence, Congenital
- Congenital Absence of Cerebral Hemispheres
- Hydranencephalies
- Hemihydranencephaly
- Hydranencephaly with Proliferative Vasculopathy
- Hemihydranencephalies
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Aspects Covered
34 allowable subheadings
Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.
MeSH Record
History Note
91(64); was see under ANENCEPHALY 1979-90; was see under ANENCEPHALUS 1967-78
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References
- National Library of Medicine. Hydranencephaly. Medical Subject Headings (MeSH). 2026. Unique ID D006832. http://id.nlm.nih.gov/mesh/2026/D006832
- Hydranencephaly. In: Wikipedia. https://en.wikipedia.org/wiki/Hydranencephaly
- Hydranencephaly. In: Wikidata. https://www.wikidata.org/wiki/Q2565270