Chemicals and Drugs

Histidine Ammonia-Lyase

An enzyme that catalyzes the first step of histidine catabolism, forming UROCANIC ACID and AMMONIA from HISTIDINE. Deficiency of this enzyme is associated with elevated levels of serum histidine and is called histidinemia (AMINO ACID METABOLISM, INBORN ERRORS).

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

An enzyme that catalyzes the first step of histidine catabolism, forming UROCANIC ACID and AMMONIA from HISTIDINE. Deficiency of this enzyme is associated with elevated levels of serum histidine and is called histidinemia (AMINO ACID METABOLISM, INBORN ERRORS).

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Classification

Broader headings

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MeSH Record

Synonyms

9 entry terms
  • Histidase
  • Histidinase
  • Histidine Deaminase
  • Histidine alpha-Deaminase
  • Ammonia-Lyase, Histidine
  • Deaminase, Histidine
  • Histidine Ammonia Lyase
  • Histidine alpha Deaminase
  • alpha-Deaminase, Histidine

MeSH Record

Aspects Covered

29 allowable subheadings

Indexed with the subheadings administration & dosage, adverse effects, analysis, antagonists & inhibitors, biosynthesis, blood, cerebrospinal fluid, chemical synthesis, chemistry, classification, deficiency, drug effects, economics, genetics, history, immunology, isolation & purification, metabolism, pharmacokinetics, pharmacology, physiology, poisoning, radiation effects, standards, supply & distribution, therapeutic use, toxicity, ultrastructure, urine.

MeSH Record

Indexing Annotation

/defic: consider also histidinemia (AMINO ACID METABOLISM, INBORN ERRORS)

MeSH Record

History Note

98(73)

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AMA Style

References

  1. National Library of Medicine. Histidine Ammonia-Lyase. Medical Subject Headings (MeSH). 2026. Unique ID D006638. http://id.nlm.nih.gov/mesh/2026/D006638
  2. Histidine Ammonia-Lyase. In: Wikidata. https://www.wikidata.org/wiki/Q24725629