Chemicals and Drugs

Ferrochelatase

A mitochondrial enzyme found in a wide variety of cells and tissues. It is the final enzyme in the 8-enzyme biosynthetic pathway of HEME. Ferrochelatase catalyzes ferrous insertion into protoporphyrin IX to form protoheme or heme. Deficiency in this enzyme results in ERYTHROPOIETIC PROTOPORPHYRIA.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A mitochondrial enzyme found in a wide variety of cells and tissues. It is the final enzyme in the 8-enzyme biosynthetic pathway of HEME. Ferrochelatase catalyzes ferrous insertion into protoporphyrin IX to form protoheme or heme. Deficiency in this enzyme results in ERYTHROPOIETIC PROTOPORPHYRIA.

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Classification

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See Also

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Synonyms

10 entry terms
  • Heme Synthetase
  • Porphyrin-Metal Chelatase
  • Protoheme Ferro-Lyase
  • Chelatase, Porphyrin-Metal
  • Ferro-Lyase, Protoheme
  • Porphyrin Metal Chelatase
  • Protoheme Ferro Lyase
  • Synthetase, Heme
  • Zinc Chelatase
  • Chelatase, Zinc

MeSH Record

Aspects Covered

28 allowable subheadings

Indexed with the subheadings administration & dosage, adverse effects, analysis, antagonists & inhibitors, biosynthesis, blood, cerebrospinal fluid, chemical synthesis, chemistry, classification, drug effects, economics, genetics, history, immunology, isolation & purification, metabolism, pharmacokinetics, pharmacology, physiology, poisoning, radiation effects, standards, supply & distribution, therapeutic use, toxicity, ultrastructure, urine.

MeSH Record

History Note

1991(1977); use LYASES 1977-1990

MeSH Record

Previous Indexing

  • Iron (1966-1976)
  • Lyases (1966-1976)
  • Porphyrins (1966-1976)
  • Protoporphyrins (1975-1976)

MeSH Hierarchy

Tree Numbers

AMA Style

References

  1. National Library of Medicine. Ferrochelatase. Medical Subject Headings (MeSH). 2026. Unique ID D005294. http://id.nlm.nih.gov/mesh/2026/D005294
  2. Ferrochelatase. In: Wikidata. https://www.wikidata.org/wiki/Q24770752