Diseases

Dermatofibrosarcoma

A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA.

MeSH Record

Classification

Broader headings

Related Concepts

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MeSH Record

Synonyms

76 entry terms
  • Darier-Ferrand Tumor
  • Darier-Hoffmann Tumor
  • Dermatofibrosarcoma Protuberan
  • Darier Ferrand Tumor
  • Darier Hoffmann Tumor
  • Dermatofibrosarcoma Protuberans
  • Dermatofibrosarcomas
  • Protuberan, Dermatofibrosarcoma
  • Protuberans, Dermatofibrosarcoma
  • Tumor, Darier-Ferrand
  • Tumor, Darier-Hoffmann
  • Bednar Tumor
  • Bednar's Tumor
  • DFSP, Fibrosarcomatous
  • DFSP, Juvenile
  • DFSP, Myxoid
  • DFSP, Pigmented
  • Dermatofibrosarcoma Protuberans, Familial
  • Dermatofibrosarcoma Protuberans, Fibrosarcomatous
  • Dermatofibrosarcoma Protuberans, Giant Cell
  • Dermatofibrosarcoma Protuberans, Myxoid
  • Dermatofibrosarcoma Protuberans, Pigmented
  • FS-DFSP
  • Familial Dermatofibrosarcoma Protuberans
  • Fibrosarcomatous Dermatofibrosarcoma Protuberans
  • Giant Cell Fibroblastoma
  • Giant Dermatofibrosarcoma Protuberans
  • Metastatic Dermatofibrosarcoma Protuberans
  • Bednars Tumor
  • Cell Fibroblastoma, Giant
  • Cell Fibroblastomas, Giant
  • DFSPs, Fibrosarcomatous
  • DFSPs, Juvenile
  • DFSPs, Myxoid
  • DFSPs, Pigmented
  • Dermatofibrosarcoma Protuberan, Familial
  • Dermatofibrosarcoma Protuberan, Fibrosarcomatous
  • Dermatofibrosarcoma Protuberan, Giant
  • Dermatofibrosarcoma Protuberan, Metastatic
  • Dermatofibrosarcoma Protuberan, Myxoid
  • Dermatofibrosarcoma Protuberan, Pigmented
  • Dermatofibrosarcoma Protuberans, Giant
  • Dermatofibrosarcoma Protuberans, Metastatic
  • Familial Dermatofibrosarcoma Protuberan
  • Fibroblastoma, Giant Cell
  • Fibroblastomas, Giant Cell
  • Fibrosarcomatous DFSP
  • Fibrosarcomatous DFSPs
  • Fibrosarcomatous Dermatofibrosarcoma Protuberan
  • Giant Cell Fibroblastomas
  • Giant Dermatofibrosarcoma Protuberan
  • Juvenile DFSP
  • Juvenile DFSPs
  • Metastatic Dermatofibrosarcoma Protuberan
  • Myxoid DFSP
  • Myxoid DFSPs
  • Myxoid Dermatofibrosarcoma Protuberan
  • Myxoid Dermatofibrosarcoma Protuberans
  • Pigmented DFSP
  • Pigmented DFSPs
  • Pigmented Dermatofibrosarcoma Protuberan
  • Pigmented Dermatofibrosarcoma Protuberans
  • Protuberan, Familial Dermatofibrosarcoma
  • Protuberan, Fibrosarcomatous Dermatofibrosarcoma
  • Protuberan, Giant Dermatofibrosarcoma
  • Protuberan, Metastatic Dermatofibrosarcoma
  • Protuberan, Myxoid Dermatofibrosarcoma
  • Protuberan, Pigmented Dermatofibrosarcoma
  • Protuberans, Familial Dermatofibrosarcoma
  • Protuberans, Fibrosarcomatous Dermatofibrosarcoma
  • Protuberans, Giant Dermatofibrosarcoma
  • Protuberans, Metastatic Dermatofibrosarcoma
  • Protuberans, Myxoid Dermatofibrosarcoma
  • Protuberans, Pigmented Dermatofibrosarcoma
  • Tumor, Bednar
  • Tumor, Bednar's

MeSH Record

Aspects Covered

39 allowable subheadings

Indexed with the subheadings blood, blood supply, cerebrospinal fluid, chemically induced, chemistry, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, secondary, surgery, therapy, ultrastructure, urine, veterinary, virology.

MeSH Record

Indexing Annotation

coordinate with with SKIN NEOPLASMS

MeSH Record

History Note

94

MeSH Record

Previous Indexing

  • Fibrosarcoma (1966-1993)
  • Skin Neoplasms (1966-1993)

MeSH Hierarchy

Tree Numbers

AMA Style

References

  1. National Library of Medicine. Dermatofibrosarcoma. Medical Subject Headings (MeSH). 2026. Unique ID D018223. http://id.nlm.nih.gov/mesh/2026/D018223
  2. Dermatofibrosarcoma. In: Wikipedia. https://en.wikipedia.org/wiki/Dermatofibrosarcoma_protuberans
  3. Dermatofibrosarcoma. In: Wikidata. https://www.wikidata.org/wiki/Q1200239