Diseases

Congenital Ichthyosiform Erythroderma

Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.

MeSH Record

Classification

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MeSH Record

Synonyms

7 entry terms
  • Erythroderma, Congenital Ichthyosiform
  • Ichthyosiform Erythroderma, Congenital
  • Congenital Ichthyosiform Erythrodermas
  • Erythrodermas, Congenital Ichthyosiform
  • Ichthyosiform Erythrodermas, Congenital
  • Congenital Ichthyosiform Erythroderma, Dry Type
  • Congenital Ichthyosiform Erythroderma, Wet Type

MeSH Record

Aspects Covered

34 allowable subheadings

Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.

MeSH Record

Indexing Annotation

an ichthyosis rather than an erythroderma; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES

MeSH Record

History Note

91

MeSH Record

Previous Indexing

  • Ichthyosis (1966-1990)

MeSH Hierarchy

Tree Numbers

  1. C16w.131w.831.512w.400w
  2. C16w.320w.850w.400w
  3. C16w.614.492w.400w
  4. C17.800w.428w.333w.250w
  5. C17.800w.804.512w.400w
  6. C17.800w.827w.400w

AMA Style

References

  1. National Library of Medicine. Congenital Ichthyosiform Erythroderma. Medical Subject Headings (MeSH). 2026. Unique ID D016113. http://id.nlm.nih.gov/mesh/2026/D016113
  2. Congenital Ichthyosiform Erythroderma. In: Wikipedia. https://en.wikipedia.org/wiki/Congenital_ichthyosiform_erythroderma
  3. Congenital Ichthyosiform Erythroderma. In: Wikidata. https://www.wikidata.org/wiki/Q3731836