Structured Summary
Abstract
An hereditary hemolytic uremic syndrome associated with variations in the gene that encodes COMPLEMENT FACTOR H, or the related proteins CFHR1 and CFHR3. Disease often progresses to CHRONIC KIDNEY FAILURE without the prodromal symptoms of ENTEROCOLITIS and DIARRHEA that characterize typical hemolytic uremic syndrome.
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Synonyms
20 entry terms
- Atypical Hemolytic-Uremic Syndrome
- Hemolytic Uremic Syndrome, Atypical
- Non-Shiga-Like Toxin-Associated HUS
- Non-Stx-Hus
- Nonenteropathic HUS
- Atypical Hemolytic-Uremic Syndromes
- HUS, Non-Shiga-Like Toxin-Associated
- HUS, Nonenteropathic
- HUSs, Non-Shiga-Like Toxin-Associated
- HUSs, Nonenteropathic
- Hemolytic-Uremic Syndrome, Atypical
- Hemolytic-Uremic Syndromes, Atypical
- Non Shiga Like Toxin Associated HUS
- Non Stx Hus
- Non-Shiga-Like Toxin-Associated HUSs
- Nonenteropathic HUSs
- Syndrome, Atypical Hemolytic-Uremic
- Syndromes, Atypical Hemolytic-Uremic
- Toxin-Associated HUS, Non-Shiga-Like
- Toxin-Associated HUSs, Non-Shiga-Like
MeSH Record
Aspects Covered
35 allowable subheadings
Indexed with the subheadings blood, cerebrospinal fluid, chemically induced, classification, complications, congenital, diagnosis, diagnostic imaging, diet therapy, drug therapy, economics, embryology, enzymology, epidemiology, ethnology, etiology, genetics, history, immunology, metabolism, microbiology, mortality, nursing, parasitology, pathology, physiopathology, prevention & control, psychology, radiotherapy, rehabilitation, surgery, therapy, urine, veterinary, virology.
MeSH Record
History Note
2015; use Hemolytic-Uremic Syndrome 2010-2014
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AMA Style
References
- National Library of Medicine. Atypical Hemolytic Uremic Syndrome. Medical Subject Headings (MeSH). 2026. Unique ID D065766. http://id.nlm.nih.gov/mesh/2026/D065766
- Atypical Hemolytic Uremic Syndrome. In: Wikipedia. https://en.wikipedia.org/wiki/Atypical_hemolytic_uremic_syndrome
- Atypical Hemolytic Uremic Syndrome. In: Wikidata. https://www.wikidata.org/wiki/Q17165460