Chemicals and Drugs

5-Aminolevulinate Synthetase

An enzyme of the transferase class that catalyzes condensation of the succinyl group from succinyl coenzyme A with glycine to form delta-aminolevulinate. It is a pyridoxyal phosphate protein and the reaction occurs in mitochondria as the first step of the heme biosynthetic pathway. The enzyme is a key regulatory enzyme in heme biosynthesis. In liver feedback is inhibited by heme. EC 2.3.1.37.

National Library of MedicineMedical Subject Headings2026

Structured Summary

Abstract

An enzyme of the transferase class that catalyzes condensation of the succinyl group from succinyl coenzyme A with glycine to form delta-aminolevulinate. It is a pyridoxyal phosphate protein and the reaction occurs in mitochondria as the first step of the heme biosynthetic pathway. The enzyme is a key regulatory enzyme in heme biosynthesis. In liver feedback is inhibited by heme. EC 2.3.1.37.

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Classification

Broader headings

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MeSH Record

Synonyms

15 entry terms
  • 5-Aminolevulinate Synthase
  • Aminolevulinic Acid Synthetase
  • delta-Aminolevulinate Synthase
  • delta-Aminolevulinic Acid Synthetase
  • 5 Aminolevulinate Synthase
  • 5 Aminolevulinate Synthetase
  • Acid Synthetase, Aminolevulinic
  • Acid Synthetase, delta-Aminolevulinic
  • Synthase, 5-Aminolevulinate
  • Synthase, delta-Aminolevulinate
  • Synthetase, 5-Aminolevulinate
  • Synthetase, Aminolevulinic Acid
  • Synthetase, delta-Aminolevulinic Acid
  • delta Aminolevulinate Synthase
  • delta Aminolevulinic Acid Synthetase

MeSH Record

Aspects Covered

29 allowable subheadings

Indexed with the subheadings administration & dosage, adverse effects, analysis, antagonists & inhibitors, biosynthesis, blood, cerebrospinal fluid, chemical synthesis, chemistry, classification, deficiency, drug effects, economics, genetics, history, immunology, isolation & purification, metabolism, pharmacokinetics, pharmacology, physiology, poisoning, radiation effects, standards, supply & distribution, therapeutic use, toxicity, ultrastructure, urine.

MeSH Record

History Note

98(72)

MeSH Record

Previous Indexing

  • Acyltransferases (1966-1971)

MeSH Hierarchy

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AMA Style

References

  1. National Library of Medicine. 5-Aminolevulinate Synthetase. Medical Subject Headings (MeSH). 2026. Unique ID D000624. http://id.nlm.nih.gov/mesh/2026/D000624
  2. 5-Aminolevulinate Synthetase. In: Wikidata. https://www.wikidata.org/wiki/Q76539507